Dilemmas in Haemophilia

Dilemmas in Haemophilia

Feedback This is a discussion about possible factors and strategies to consider and should not be used as a guideline for clinical practice. Always discuss complicated cases with the attending H&T consultant. 00:52 Intro 01:30 Case 1: 41M Severe Haemophilia A, acute MI needing PCI Try the 4 steps! Bleeding RiskAnticoagulant characteristicsIntensity of anticoagulant (prophylactic vs therapeutic)Duration of anticoagulant therapy11:20 Cardiac Disease in Haemophilia: thoughts and consideratio...

Jaksot(23)

Haemophilia B, Gene Therapy

Haemophilia B, Gene Therapy

Feedback Timestamps to follow! 'Basics to Brilliance: Haematology Podcast' has been accredited for CPD credit by the Royal College of Pathologists UK. Medical professionals and clinical scientists ...

11 Huhti 50min

Acquired Haemophilia A

Acquired Haemophilia A

Feedback 00:52 Intro and chuckles 01:40 Case study: 75M, left calf swelling, put on DOAC, 24 hrs later haematoma and deep bleed on CT 06:00 General information Elderly (>65), Mortality 8-40%Common pre...

25 Tammi 42min

Haemophilia A in Pregnancy

Haemophilia A in Pregnancy

Feedback 00:52 Intro - very important topic 02:00 Case Study: Haem/Obstetrics clinic, Family Hx Severe Haemophilia A, 12wks pregnant 04:15 Clotting changes in pregnancy Increased: FVII, FVIII, FX, VWF...

11 Tammi 50min

Haemophilia A: Inhibitors

Haemophilia A: Inhibitors

Feedback 00:52 Intro 02:10 Definition Common: Alloantibody neutralizes FVIIIRare: causes increased clearance of FVIII1/3 of Severe Haemophilia A patientsMedian time 10-15 emergency dosesRF: Mutation t...

30 Marras 202553min

Haemophilia A: Management Basics

Haemophilia A: Management Basics

Feedback 00:52 Intro 02:35 Structure of Haemophilia A care 05:10 Key aspects of management (On-demand vs prophylaxis) 07:00 Prophylaxis: reduce death rates from ICH and reducing joint bleeds - Primary...

16 Marras 20251h 24min

Haemophilia A: Diagnosis & Investigations

Haemophilia A: Diagnosis & Investigations

Feedback 00:52 Intro 02:00 What is Haemophilia A? 03:00 Factor VIII, Pathogenesis of Haemophilia A 07:10 Structure of Factor VIII (exam pearl) 300kDHeavy (A1 A2, B) + Light Chain (A3, C1, C2) bound by...

9 Marras 202549min

Factor XIII (13), Fibrinolysis & Thrombolysis

Factor XIII (13), Fibrinolysis & Thrombolysis

Feedback 01:45 Case: Neonate with repeated umblical bleeding. IC haemorrhage. Normal Factors (so far), Normal VW screen, Normal FBC and normal film. 05:35 Factor XIII (13): function and presentations...

12 Heinä 202546min

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